Journal Article

Sudden cardiac death in Andersen–Tawil syndrome

Stefan Peters, Eric Schulze-Bahr, Susan P. Etheridge and Martin Tristani-Firouzi

in EP Europace

Published on behalf of European Heart Rhythm Association of the European Society of Cardiology (ESC)

Volume 9, issue 3, pages 162-166
Published in print March 2007 | ISSN: 1099-5129
Published online February 2007 | e-ISSN: 1532-2092 | DOI: http://dx.doi.org/10.1093/europace/eul188
Sudden cardiac death in Andersen–Tawil syndrome

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Andersen–Tawil syndrome (ATS) is an autosomal dominant or sporadic disorder characterized by periodic paralysis, dysmorphic features, and ventricular arrhythmias. Although ventricular tachycardia burden is quite high sudden cardiac death in ATS is rare. We describe a case with sudden cardiac death due to electrical storm a few days after ICD implantation in KCNJ2 mutation-negative ATS.

Keywords: Cardiac arrest; Bidirectional ventricular tachycardia; Polymorphic ventricular tachycardia; Genetic disorder; KCNJ2 mutation-negative

Journal Article.  1589 words.  Illustrated.

Subjects: Cardiovascular Medicine

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