Chapter

The Hereditary Neuropathies

Steven Herskovitz

in Peripheral Neuropathies in Clinical Practice

Published on behalf of Oxford University Press

Published in print November 2008 | ISBN: 9780195183269
Published online April 2013 | e-ISBN: 9780199322947 | DOI: http://dx.doi.org/10.1093/med/9780195183269.003.0014

Series: CONTEMP NEURO

The Hereditary Neuropathies

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In considering and classifying the hereditary neuropathies, it is useful to first distinguish those related to primary or isolated degeneration of peripheral neural elements, either alone or in association with other parts of the nervous system (system atrophies), from those where neuropathy is part of a more generalized systemic/metabolic process (also called syndromic hereditary neuropathies). For the nonsystemic inherited neuropathies, classification follows involvement of specific neuron or nerve fiber types: motor and sensory nerves (HMSN or CMT), sensory and autonomic nerves (HSAN), lower motor neurons or nerves (dHMN), cerebellum and large-diameter sensory neurons (SCA), and spinal pyramidal tracts and lower motor neurons or nerves (HSP or SPG) (Table 14–1).1

Chapter.  23637 words.  Illustrated.

Subjects: Neurology

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