One of a group of rare hereditary disorders (known as the neuronal ceroid lipofuscinoses) that also includes Tay-Sachs disease. Fatty substances accumulate in the cells of the nervous system, causing progressive dementia, epilepsy, spasticity, and visual failure. The condition starts in late infancy or childhood. There is no treatment. F. E. Batten (1865–1918), British neurologist
Subjects: Medicine and Health.